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dc.contributor.authorRocha, Julio Cesar
dc.contributor.authorvan Rijn, Margreet
dc.contributor.authorvan Dam, Esther
dc.contributor.authorAhring, Kirsten
dc.contributor.authorBelanger-Quintana, Amaya
dc.contributor.authorDokoupil, Katharina
dc.contributor.authorOzel, Hulya Gokmen
dc.contributor.authorLammardo, Anna Maria
dc.contributor.authorRobert, Martine
dc.contributor.authorHeidenborg, Carina
dc.contributor.authorMacDonald, Anita
dc.date.accessioned2019-12-19T06:13:59Z
dc.date.available2019-12-19T06:13:59Z
dc.date.issued2016
dc.identifier.issn0250-6807
dc.identifier.urihttps://doi.org/10.1159/000442304
dc.identifier.urihttp://hdl.handle.net/11655/20783
dc.description.abstractBackground: Severe intellectual disability and growth impairment have been overcome by the success of early and continuous treatment of patients with phenylketonuria (PKU). However, there are some reports of obesity, particularly in women, suggesting that this may be an important comorbidity in PKU. It is becoming evident that in addition to acceptable blood phenylalanine control, metabolic dieticians should regard weight management as part of routine clinical practice. Summary: It is important for practitioners to differentiate the 3 levels for overweight interpretation: anthropometry, body composition and frequency and severity of associated metabolic comorbidities. The main objectives of this review are to suggest proposals for the minimal standard and gold standard for the assessment of weight management in PKU. While the former aims to underline the importance of nutritional status evaluation in every specialized clinic, the second objective is important in establishing an understanding of the breadth of overweight and obesity in PKU in Europe. Key Messages: In PKU, the importance of adopting a European nutritional management strategy on weight management is highlighted in order to optimize long-term health outcomes in patients with PKU. (C) 2015 S. Karger AG, Basel
dc.language.isoen
dc.publisherKarger
dc.relation.isversionof10.1159/000442304
dc.rightsinfo:eu-repo/semantics/openAccess
dc.subjectEndocrinology & Metabolism
dc.subjectNutrition & Dietetics
dc.titleWeight Management In Phenylketonuria: What Should Be Monitored?
dc.typeinfo:eu-repo/semantics/review
dc.typeinfo:eu-repo/semantics/publishedVersion
dc.relation.journalAnnals Of Nutrition And Metabolism
dc.contributor.departmentBeslenme ve Diyetetik
dc.identifier.volume68
dc.identifier.issue1
dc.identifier.startpage60
dc.identifier.endpage65
dc.indexingWoS
dc.indexingScopus


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