Now showing items 1-2 of 2
Weight Management In Phenylketonuria: What Should Be Monitored?
Background: Severe intellectual disability and growth impairment have been overcome by the success of early and continuous treatment of patients with phenylketonuria (PKU). However, there are some reports of obesity, ...
Adjusting Diet With Sapropterin In Phenylketonuria: What Factors Should Be Considered?
(CambrAdge Uni^ Press, 2011)
The usual treatment for phenylketonuria (PKU) is a phenylalanine-restricted diet. Following this diet is challenging, and long-term adherence (and hence metabolic control) is commonly poor. Patients with PKU (usually, but ...